ACAA1

3-Ketoacyl-CoA thiolase, peroxisomal also known as acetyl-Coenzyme A acyltransferase 1 is an is_associated_with::enzyme that in humans is encoded by the ACAA1 is_associated_with::gene.

Acetyl-Coenzyme A acyltransferase 1 is an is_associated_with::acetyl-CoA C-acyltransferase enzyme.

Function
This gene encodes an enzyme operative in the is_associated_with::beta oxidation system of the is_associated_with::peroxisomes.

Clinical significance
Deficiency of this enzyme leads to pseudo-is_associated_with::Zellweger syndrome.