Galactosylceramidase

Galactosylceramidase (or galactocerebrosidase) is an is_associated_with::enzyme that in humans is encoded by the GALC is_associated_with::gene. Galactosylceramidase is an enzyme which removes is_associated_with::galactose from is_associated_with::ceramide derivatives (is_associated_with::galactocerebrosides).

Galactosylceramidase is a is_associated_with::lysosomal protein which hydrolyzes the is_associated_with::galactose ester bonds of is_associated_with::galactocerebroside, galactosylsphingosine, is_associated_with::lactosylceramide, and monogalactosyldiglyceride. Mutations in this gene have been associated with is_associated_with::Krabbe disease, also known as globoid cell leukodystrophy.